Sodium Phenylbutyrate
Sodium phenylbutyrate is used together with a proper diet to help treat urea cycle disorders, including carbamylphosphate synthetase deficiency (CPS), ornithine transcarbamylase deficiency (OTC), or argininosuccinate synthetase (AS)
Systematic Name
4-phenylbutyric acid, sodium salt
Brand Name(S)
Buphenyl
Therapeutic Category
Hyperammonemia
Suitable Formulations
Solid
Approvals
US DMF
EU-WC